Ad
related to: aorta disease and marfan syndromewexnermedical.osu.edu has been visited by 10K+ users in the past month
Search results
Results From The WOW.Com Content Network
As people with Marfan syndrome live longer, other vascular repairs are becoming more common, e.g., repairs of descending thoracic aortic aneurysms and aneurysms of vessels other than the aorta. [citation needed] The skeletal and ocular manifestations of Marfan syndrome can also be serious, although not life-threatening.
The Bentall procedure is a type of cardiac surgery involving composite graft replacement of the aortic valve, aortic root, and ascending aorta, with re-implantation of the coronary arteries into the graft. This operation is used to treat combined disease of the aortic valve and ascending aorta, including lesions associated with Marfan syndrome.
With Marfan syndrome patients, they must have their aorta monitored with regular imaging to detect a dilation or an aneurysm, signs that a dissection could be impending. "It's common to have ...
What is Marfan syndrome? This genetic disorder of the connective tissue impacts heart health. Causes long bones. People have long arms, legs.
Connective tissue disorders such as Marfan syndrome, Ehlers–Danlos syndrome, and Loeys–Dietz syndrome increase the risk of aortic dissection. [13] Similarly, vasculitides such as Takayasu's arteritis , giant cell arteritis , polyarteritis nodosa , and Behçet's disease have been associated with a subsequent aortic dissection.
Familial thoracic aortic aneurysm is an autosomal dominant [1] disorder of large arteries. There is an association between familial thoracic aortic aneurysm and Marfan syndrome as well as other hereditary connective tissue disorders.
Additional factors that contribute to this condition include osteogenesis imperfecta, inflammatory aortic diseases, intrinsic valve disease, Loeys-Dietz syndrome, Marfan syndrome, and operated congenital heart disease. [3] On a gross level, there is a pear-shaped, symmetric enlargement due to proximal aortic dilation.
The principal causes of death due to thoracic aneurysmal disease are dissection and rupture. Once rupture occurs, the mortality rate is 50–80%. Most deaths in patients with Marfan syndrome are the result of aortic disease. [citation needed]